Top 5 Unknown or Little Know Hearing Problems or Disorders

If the eyes are visual gateway to the soul as the old saying goes, the ears may easily be a gateway to physical health. Most of the time Doctor detect the major problem in our body by just only by seeing our hearing health. The most severe diseases such as nausea and dizziness to paralysis and even death, can be easily detected by health of our ears only. In this post we will discuss the most unknown ear disorders which can go undetected manually. You need to take the help of the best ENT specialist Gurgaon for proper diagnosis and treatment. Below is the list of the most unknown eye disorder. Checkout whether you are victim of the same or not.

Superior semicircular canal dehiscence syndrome (SCDS)

Structures in the inner part of the ear are very fine. Even a mustard size hole in a bone in the inner part of the ear can create severe balance disorders which can leads to other major problems such as problem in walking, turning head to look behind them. This is one of the major problem seen in 1 out of million people. The major symptoms of such are own voices or the sound of their pulse are too loud and in most severe case, the patient can hear the sound of his own eyes moving.

Diagnosis and treatment

The ENT specialist can advised you for CT scan of the inner part of the ear for any abnormal opening in temporal bone covering the superior canal. If the problem is detected then the ENT doctor can also suggest for surgery for corrective measures. Surgical risks include hearing loss and nerve damage; rehabilitation is required as the inner ear heals and the brain adjusts.

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The second most uncommon condition called Cholesteatoma affects one in million people. The cyst-like growth develops in the inner part of the ear. It will also leads to permanent deafness and other serious problem such as meningitis if left undiagnosed. The Symptoms can include a smelly discharge and hearing loss.

There are two types of cholesteatoma are:

Congenital cholesteatoma, which grows behind the eardrum and generally occurs during time of birth. Medical professionals detected that this condition occurs when skin cells grow in the wrong place. Acquired cholesteatoma, which usually occurs only in adults, often those who have chronic or recurring ear infections.

Diagnosis and treatment

Fortunately, ENT specialists can see this white mass when they detect the ear. Most cholesteatomas can be removed with the help of surgery. If it left without any treatment then it may leads to permanent damage to structures of the inner ear resulting in dizziness and balance problems or interfere with facial nerves and muscles, causing paralysis. Since cholesteatoma is often infected, the toxicity can spread to other parts of the body, causing meningitis and brain abscesses in rare cases.

Autoimmune inner ear disease (AIED)

The rarest of all ear syndrome, which is caused by antibodies or immune cells which attack on the inner part of the ear which include progressive hearing loss with accompanying dizziness. Theories as to its causes range from a delayed response by the immune system after damage to the inner ear, to accidental damage caused by antibodies fighting a threat, to genetic factors.

Diagnosis and treatment

It is accounts for only one percent in all the hearing losses and can only be detected by multiple series of hearing tests and blood tests for common autoimmune disease. Although it is considered as a chronic, incurable disorder which causes permanent damage to hearing and balance, its symptoms can be managed. The treatments of AIED includes the the use of steroids and other medications, cell and gene therapy and cochlear implant surgery.

Meniere’s disease

It is sometimes called as endolymphatic hydrops, include vertigo, tinnitus, a feeling of fullness or pressure in the ear and fluctuating hearing loss. Meniere’s disease is unilateral, meaning it only affects one ear, and ony occurs between the ages of 20 and 50. Medical professionals aren’t sure exactly what causes the disease, but many believe it’s the result of an abnormal amount of fluid in the inner ear. It is estimated to affect one out of every 1,000 people.

Diagnosis and treatment

Diagnosis for the disease typically includes hearing and balance assessments and occasionally blood tests to rule out other disorders. Meniere’s disease is considered a chronic condition, there are treatments which can minimize the discomfort and disruption of daily activities. Commonly prescribed medications include those for motion sickness and nausea. Other therapies which have proven successful include vestibular rehabilitation to improve balance, wearing a hearing aid and the use of a Meniett pulse generator which applies pulses of pressure to the ear canal through a ventilation tube.

Crohn’s disease

The disease is usually associated with swelling and irritation of the digestive tract, doctors recently discovered it can also affect other parts of your body. In July 2018, a 10-year-old boy was diagnosed with Crohn’s disease after he had suffered from ear pain and hearing problems for years. His ear troubles and bloody ear discharge were treated unsuccessfully with ear drops, antibiotics and other medications. Doctors had no reason to suspect he had Crohn’s disease because he didn’t have any stomach issues. It wasn’t until he was finally diagnosed with Crohn’s disease and prescribed medication that his ear problems were resolved.


These hearing and ear disorders are very rare and your chances of developing them are slim. Even so, you are always the best advocate for your personal health. Find a hearing health professional you can trust and schedule hearing evaluations on a regular basis. Be honest with your doctor and inform them of any family history involving ear disorders or other medical information. Becoming an educated health consumer and partnering with your hearing healthcare professional goes a long way toward identifying potential health problems as they occur so you can continue to lead an active, healthy life


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Dr Rudra Prakash Rai
Dr Rudra Prakash Rai


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